SINDROM WEST (SPASME INFATILE)

  • Elvina Zuhir Universitas Abdurrab

Abstract

Infantile spasms are an age-appropriate epilepsy syndrome characterized by flexion, extension, and combined flexion-extension spasms that often occur simultaneously. This study may aim to identify the characteristics of infantile spasms in terms of clinical symptoms, electroencephalogram (EEG) findings, and other diagnostic tests. The development of more accurate diagnostic methods can assist in early recognition and further treatment. The results of the MRI examination showed: signs of mild cerebral atrophy were accompanied by mild myelination disorders with pathological hyper-intensity in the periventricular subcortical white matter in the pre-central / posterior frontal lobe area bilaterally, other than that other supratentorial cerebral structures did not show further abnormalities, especially in the absence of SOL, congenital anomaly, hemorrhage, cerebral dystrophy/sclerosis / malacia or other pathological intensity both supra and infra-tentorial, including in the temporal lobe and hippocampus bilaterally.

Keywords: infantile spasms, flexion spasms

References

[1] Curatolo P. Infantile Spasms (West’sSyndrome). Maria B editor. In: Current Management in Child Neurology. 3th ed. BC Decker Inc: 2005.p.134-8
[2] Exil G. Kejang. Dalam: Schwartz M editor. Pedoman Klinis Pediatri. Pendit B, Hartawan B, Iqbal M, Yurita alih bahasa. Jakarta: Penerbit Buku Kedokteran EGC; 2005.p.664-6
[3] Guerrini R and Pellacani S. Infantile Spasms and West Syndrome: Anatomo-Electroclinical Patterns and Etiology. In: Guzzetta F, Bernardina B, Guerrini R editors. Progress in Epileptic Spasm and West Syndrome. France: Editions John Libbey Eurotext; 2007.p.26- 37
[4] Dulac O, Ballaban K, Moshe S. West Syndrome. 2003.
Tersedia:http://www.ilae-epilepsy.org/ctf/west_syndrome.html.
[5] Marsh ED and Golden JA. Developing An Animal Model for Infantile Spasms: Pathogenesis, Problems and Progress. Disease Models & Mechanisms: 2009;2.p
Published
2023-08-25
Section
Articles
PDF (Bahasa Indonesia)
Abstract views: 166
downloads: 0 PDF (Bahasa Indonesia)
Abstract views: 166
downloads: 202